UPDATE CLINICAL REVIEW
Gastrointestinal polyposis in paediatric age: an updateLavinia
1UOC Chirurgia e Endoscopia Digestiva Dipartimento Chirurgie Specialistiche Ospedale Pediatrico Bambino Gesù
Polyposis syndromes are rare but significant disorders which predispose to a lifetime risk of gastrointestinal and extra-intestinal cancers, also in paediatric age. In 2019 the European Society for Paediatric Gastroenterology, Hepatology and Nutrition provided recommendations regarding the management of these syndromes. Recently, specific genotype-phenotype correlations have been found, which should lead to more individualised surveillance recommendations.