Pediatric Hepatology
“New” autoimmune liver diseases
Marco Sciveres
Epatologia Pediatrica e Trapianto di Fegato. IRCCS ISMETT, University of Pittsburgh Medical Center Italy. Palermo
The spectrum of autoimmune liver diseases comprehends several entities, some of them were described in the last two decades. Small-duct sclerosing cholangitis shares clinical and histological features with primary sclerosing cholangitis but shows a normal cholangiographic picture. Altough similar to classical sclerosing cholangitis it presents some important peculiarities. Also IgG4-related was recently described as a part of IgG4-related multisystemic disease.